Anti-GNS Antibody

Rs. 45,619.00
SKU stj29625

General Information

Product name Anti-GNS Antibody
Short Description Rabbit polyclonal to GNS
Description The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
Applications WB
Dilution range WB 1:500 - 1:2000
Protein Name Anti-GNS Antibody
Immunogen Recombinant fusion protein containing a sequence corresponding to amino acids 293-552 of human GNS (NP_002067.1).
Storage Instruction Store at -20℃. Avoid freeze / thaw cycles.
Type of Usage For Research Use Only (RUO).

Product Properties

Host Rabbit
Clonality Polyclonal
Reactivity
Conjugation Unconjugated
Purification Affinity purification
Isotype IgG
Formulation Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

Target

Gene ID
Gene Symbol
Molecular Weight 62.1 kDa
Database Links
Alternative Names GNSN-acetylglucosamine-6-sulfatase GNS
Function
Cellular Localization Lysosome
Tissue Specificity
Swiss-Prot Key

 

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