| Product name |
Anti-GNS Antibody |
| Short Description |
Rabbit polyclonal to GNS |
| Description |
The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. |
| Applications |
WB |
| Dilution range |
WB 1:500 - 1:2000 |
| Protein Name |
Anti-GNS Antibody |
| Immunogen |
Recombinant fusion protein containing a sequence corresponding to amino acids 293-552 of human GNS (NP_002067.1). |
| Storage Instruction |
Store at -20℃. Avoid freeze / thaw cycles. |
| Type of Usage |
For Research Use Only (RUO). |
