Anti-PEX7 Antibody

Rs. 45,619.00
SKU stj29024

General Information

Product name Anti-PEX7 Antibody
Short Description Rabbit polyclonal to PEX7
Description This gene encodes the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2). Defects in this gene cause peroxisome biogenesis disorders (PBDs), which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs, with more than one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene have been associated with PBD complementation group 11 (PBD-CG11) disorders, rhizomelic chondrodysplasia punctata type 1 (RCDP1), and Refsum disease (RD).
Applications WB
Dilution range WB 1:500 - 1:2000
Protein Name Anti-PEX7 Antibody
Immunogen Recombinant fusion protein containing a sequence corresponding to amino acids 1-240 of human PEX7 (NP_000279.1).
Storage Instruction Store at -20℃. Avoid freeze / thaw cycles.
Type of Usage For Research Use Only (RUO).

Product Properties

Host Rabbit
Clonality Polyclonal
Reactivity
Conjugation Unconjugated
Purification Affinity purification
Isotype IgG
Formulation Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

Target

Gene ID
Gene Symbol
Molecular Weight 35.9 kDa
Database Links
Alternative Names PEX7Peroxisomal targeting signal 2 receptor antibodyPTS2 receptor antibodyPeroxin-7PEX7 antibodyPTS2R
Function Binds to the N-terminal PTS2-type peroxisomal targeting signal and plays an essential role in peroxisomal protein import
Cellular Localization Peroxisome, Cytoplasm
Tissue Specificity Ubiquitous, highest expression in pancreas, skeletal muscle and heart
Swiss-Prot Key

 

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